Catalog

Indeterminate cell histiocytosis

2B31.6

Link to WHO Definition

Indeterminate cell histiocytosis – http://id.who.int/icd/entity/583219258

A very rare dendritic cell tumour composed of spindle to ovoid cells with a phenotype that is similar to the Langerhans cells. Patients usually present with cutaneous papules, nodules, and plaques. Systemic symptoms are usually absent. The clinical course is variable.

Parents