Catalog

Thiemann disease, familial form

No MMS code

Link to WHO Definition

Thiemann disease, familial form – http://id.who.int/icd/entity/67016273

Thiemann disease is a very rare genetic necrotic bone disorder characterised clinically by painless swelling of the proximal interphalangeal joints associated with osteonecrosis of epiphyses followed by osteoarthritic changes, with onset before 25 years of age and often a benign course.