Catalog

Pulmonary manifestations of atypical cystic fibrosis

No MMS code

Link to WHO Definition

Pulmonary manifestations of atypical cystic fibrosis – http://id.who.int/icd/entity/670879513

This refers to pulmonary manifestations in an atypical autosomal recessive genetic disorder that affects most critically the lungs, and also the pancreas, liver, and intestine. It is characterised by abnormal transport of chloride and sodium across an epithelium, leading to thick, viscous secretions.