Catalog
Neuronal intranuclear inclusion disease
No MMS code
Link to WHO Definition
Neuronal intranuclear inclusion disease – http://id.who.int/icd/entity/693937860
Neuronal intranuclear inclusion disease is a very rare multisystem neurodegenerative disorder characterised by the presence of eosinophilic intranuclear inclusions in neuronal and glial cells, and neuronal loss. Infantile, juvenile, and adult-onset cases have been described.