Catalog

Hepatic veno-occlusive disease - immunodeficiency syndrome

4A01.33

Link to WHO Definition

Hepatic veno-occlusive disease - immunodeficiency syndrome – http://id.who.int/icd/entity/712514250

Hepatic veno-occlusive disease - immunodeficiency syndrome is characterised by the association of severe hypogammaglobulinemia, combined T and B cell immunodeficiency, absent lymph node germinal centres, absent tissue plasma cells and hepatic veno-occlusive disease.

Parents