Catalog

Hereditary haemorrhagic telangiectasia

LA90.00

Link to WHO Definition

Hereditary haemorrhagic telangiectasia – http://id.who.int/icd/entity/714406192

Rendu-Osler-Weber disease, also called hereditary haemorrhagic telangiectasia (HHT), is a genetic disorder of angiogenesis leading to arteriovenous dilatations: cutaneo-mucosal haemorrhagic telangiectasias and visceral shunting.

Parents