Catalog

Pancreatoblastoma

No MMS code

Link to WHO Definition

Pancreatoblastoma – http://id.who.int/icd/entity/733863058

Pancreatoblastoma is a very rare malignant epithelial neoplasm of the pancreas showing multiple lines of differentiation including acinar differentiation and squamoid nests. Endocrine and ductal differentiation, and a distinct mesenchymal component, can also be seen. Most pancreatoblastomas occur in children. Pancreatoblastoma is the most common malignant pancreatic neoplasm of childhood. It has been reported in newborns with Beckwith-Wiedemann syndrome. Grossly, pancreatoblastomas are usually large and well-demarcated, and are often palpable in children.