Catalog

Diaphyseal medullary stenosis - bone malignancy

No MMS code

Link to WHO Definition

Diaphyseal medullary stenosis - bone malignancy – http://id.who.int/icd/entity/747928135

Diaphyseal medullary stenosis with malignant fibrous histiocytoma is a very rare autosomal dominant bone dysplasia/cancer syndrome characterised clinically by bone infarctions, cortical growth abnormalities, pathological fractures, and development of bone sarcoma (malignant fibrous histiocytoma).