Catalog
Cutaneous malakoplakia
No MMS code
Link to WHO Definition
Cutaneous malakoplakia – http://id.who.int/icd/entity/782619380
Malakoplakia is a rare chronic suppurative granulomatous disorder due to inadequate bacterial killing within macrophages and monocytes. It is closely associated with impaired immunity such as seen with HIV infection, diabetes and organ transplantation. It most commonly involves the genitourinary or gastrointestinal tracts and may present with cutaneous nodules, plaques, ulcers or draining sinuses affecting particularly the vagina, vulva and perianal skin.