Catalog
Complex primary lymphoedema
No MMS code
Link to WHO Definition
Complex primary lymphoedema – http://id.who.int/icd/entity/793241368
Syndromes of which lymphoedema is a component
Parents
Children
- Lymphoedema with atrial septal defects and facial changes
- LD2F.15 Noonan syndrome
- Cholestasis - lymphoedema syndrome
- Lymphoedema, microcephaly and chorioretinopathy syndrome
- Hennekam lymphangiectasia-lymphoedema syndrome
- Deafness, lymphoedema and leukaemia syndrome
- EE11.1 Yellow nail syndrome
- Lymphoedema-distichiasis syndrome