Catalog

Von Willebrand disease type 3

No MMS code

Link to WHO Definition

Von Willebrand disease type 3 – http://id.who.int/icd/entity/805917536

Type 3 von Willebrand disease is the most severe form of VWD characterised by a bleeding disorder associated with a total or near-total absence of Willebrand factor (von Willebrand factor; VWF) in the plasma and cellular compartments, also leading to a profound deficiency of plasmatic factor VIII (FVIII). The type 3 disease is the rarest form of VWD, accounting for less than 5% of all cases.