Catalog
Congenital lipoid adrenal hyperplasia due to STAR deficiency
No MMS code
Link to WHO Definition
Congenital lipoid adrenal hyperplasia due to STAR deficiency – http://id.who.int/icd/entity/832786122
This is an endocrine disorder that is an uncommon and potentially lethal form of congenital adrenal hyperplasia (CAH). This diagnosis is due to STAR deficiency.