Catalog

Shy-Drager syndrome

No MMS code

Link to WHO Definition

Shy-Drager syndrome – http://id.who.int/icd/entity/859030797

Shy-Drager is a form of multiple system atrophy. Multiple system atrophy (MSA) is a sporadic, adult onset (mean age of onset 55-58 years) progressive (mean disease duration 7-9 years) neurodegenerative disease characterised by a variable combination of autonomic failure, parkinsonism and cerebellar signs. Neuropathological examination shows striatonigral, olivopontocerebellar and autonomic nuclei neuronal loss, gliosis, myelin pallor and axonal degeneration.