Catalog
Corpus callosum agenesis – cataract – immunodeficiency
No MMS code
Link to WHO Definition
Corpus callosum agenesis – cataract – immunodeficiency – http://id.who.int/icd/entity/908973419
Vici syndrome is characterised by the combination of agenesis of the corpus callosum, cutaneous hypopigmentation, bilateral cataract and combined immunodeficiency.