Catalog
Early-onset parkinsonism - intellectual deficit
Link to WHO Definition
Early-onset parkinsonism - intellectual deficit – http://id.who.int/icd/entity/937544163
Early-onset parkinsonism with intellectual deficit is a basal ganglia disorder characterised by parkinsonian-type symptoms (postural changes, tremor, rigidity), megalencephaly and variable intellectual deficit. Other signs are frontal bossing, persistent frontal lobe reflexes, strabismus and seizures.