Catalog
Megaloencephalic leukoencephalopathy with subcortical cysts
No MMS code
Link to WHO Definition
Megaloencephalic leukoencephalopathy with subcortical cysts – http://id.who.int/icd/entity/945878586
Megalencephalic leukoencephalopathy with subcortical cysts is a rare form of leukodystrophy characterised by early onset ataxia followed by progressive signs of pyramidal tract involvement and mental deterioration.