Catalog

Phakomatosis pigmentokeratotica

No MMS code

Link to WHO Definition

Phakomatosis pigmentokeratotica – http://id.who.int/icd/entity/960559196

Phacomatosis pigmentokeratotica is a rare syndrome defined by the association of an organoid naevus (occasionally with sebaceous differentiation), a speckled lentiginous naevus, and other extracutaneous anomalies.