Catalog
Congenital adrenocortical insufficiency
No MMS code
Link to WHO Definition
Congenital adrenocortical insufficiency – http://id.who.int/icd/entity/980033565
This is a condition in which the adrenal glands do not produce adequate amounts of steroid hormones, primarily cortisol; but may also include impaired production of aldosterone (a mineralocorticoid), which regulates sodium conservation, potassium secretion, and water retention.