Catalog
IgG4 related disease
Link to WHO Definition
IgG4 related disease – http://id.who.int/icd/entity/99883782
IgG4 related syndrome (IgG4-related disease: IgG4-RD) is a clinical disease characterised by elevated serum IgG4 concentration and tumefaction or tissue infiltration by IgG4-positive plasma cells. The diagnostic criteria for IgG4 related syndrome have been proposed, and it may be present in a certain population of patients with a wide variety of diseases, including Mikulicz disease, autoimmune pancreatitis, hypophysitis, Riedel thyroiditis, interstitial pneumonitis, interstitial nephritis, prostatitis, lymphadenopathy, retroperitoneal fibrosis, inflammatory aortic aneurysm, and inflammatory pseudo tumour.
Parents
Children
- IgG4-related ophthalmic disease
- IgG4-related pachymeningitis
- IgG4-related mesenteritis
- IgG4-related thyroid disease
- IgG4-related hepatopathy
- Cutaneous pseudolymphoma
- EK91.2 Primary cutaneous plasmacytosis
- IgG4-related sclerosing cholangitis
- IgG4-related kidney disease
- Eosinophilic angiocentric fibrosis
- IgG4-related submandibular gland disease
- IgG4-related aortitis
- Type 1 IgG4 related autoimmune pancreatitis
- IgG4-related mediastinitis
- IgG4-related dacryoadenitis and sialadenitis
- IgG4-related retroperitoneal fibrosis