80154-8

LOINC 2.82

Monolysocardiolipin/Cardiolipin [Molar ratio] in DBS

MLCL/CL DBS-sRto

Definition

  • The ratio of monolysocardiolipin to cardiolipin in dried blood spots is measured as a diagnostic test for Barth syndrome (BTHS), an X-linked, metabolic, multi-system disorder characterized by cardiomyopathy, neutropenia, myopathy, and growth delay. [PMID: 18070816]

Component

  • Monolysocardiolipin/Cardiolipin

Specimen / system

  • Bld.dot

Class

  • CHEM

Property

  • SRto

Scale

  • Qn

Related names

  • Blood; Cardio; Cardiolip; Cardiolipn; Cardiolpn; Chemistry; CL; DBS; Dried blood spot; Filter paper; FP; MLCL; Point in time; QNT; Quan; Quant; Quantitative; Random; Scrto; Substance concentration ratio; Substance ratio; WB; Whole blood

Index terms

  • Blood
  • Cardio
  • Cardiolip
  • Cardiolipn
  • Cardiolpn
  • Chemistry
  • CL
  • DBS
  • Dried blood spot
  • Filter paper
  • FP
  • MLCL
  • Point in time
  • QNT
  • Quan
  • Quant
  • Quantitative
  • Random
  • Scrto
  • Substance concentration ratio
  • Substance ratio
  • WB
  • Whole blood