1B41

ICD-11 MMS 2026-01

Acute rheumatic fever with heart involvement

Description

A disease of the cardiovascular system, caused as a result of rheumatic fever. Rheumatic heart disease is characterised by repeated inflammation with fibrinous repair. This disease may present with cardinal anatomic changes of the valve including leaflet thickening, commissural fusion, and shortening and thickening of the tendinous cords. Inflammation and valve scarring may also occur. Confirmation is by a thoracic radiography or echocardiography.

Excludes

  • BB60.0 – Rheumatic mitral valve stenosis
  • BB61.0 – Rheumatic mitral valve insufficiency
  • BB62.0 – Rheumatic mitral valve prolapse
  • BB63.0 – Rheumatic mitral stenosis with insufficiency
  • BB70.0 – Rheumatic aortic valve stenosis
  • BB71.0 – Rheumatic aortic valve insufficiency
  • BB72.0 – Rheumatic aortic stenosis with insufficiency
  • BB80.0 – Rheumatic tricuspid valve stenosis
  • BB81.0 – Rheumatic tricuspid valve insufficiency
  • BB82.0 – Rheumatic tricuspid valve stenosis with insufficiency
  • BB90.0 – Rheumatic pulmonary valve stenosis
  • BB91.0 – Rheumatic pulmonary valve insufficiency
  • BB92.0 – Rheumatic pulmonary valve stenosis with insufficiency

Exclusions from above levels

  • NE83.1 – Infection arising from device, implant or graft, not elsewhere classified

Child codes

  • 1B41.0 – Acute rheumatic pericarditis
  • 1B41.1 – Acute rheumatic endocarditis
  • 1B41.2 – Acute rheumatic myocarditis
  • 1B41.Y – Other acute rheumatic heart disease
  • 1B41.Z – Acute rheumatic heart disease, unspecified

Sibling codes

  • 1B40 – Acute rheumatic fever without mention of heart involvement
  • 1B42 – Rheumatic chorea

Foundation entity

Acute rheumatic fever with heart involvement – http://id.who.int/icd/entity/535094176

Part of: 01: Certain infectious or parasitic diseases