1B41ICD-11 MMS 2026-01
Acute rheumatic fever with heart involvement
Description
A disease of the cardiovascular system, caused as a result of rheumatic fever. Rheumatic heart disease is characterised by repeated inflammation with fibrinous repair. This disease may present with cardinal anatomic changes of the valve including leaflet thickening, commissural fusion, and shortening and thickening of the tendinous cords. Inflammation and valve scarring may also occur. Confirmation is by a thoracic radiography or echocardiography.
Excludes
BB60.0– Rheumatic mitral valve stenosisBB61.0– Rheumatic mitral valve insufficiencyBB62.0– Rheumatic mitral valve prolapseBB63.0– Rheumatic mitral stenosis with insufficiencyBB70.0– Rheumatic aortic valve stenosisBB71.0– Rheumatic aortic valve insufficiencyBB72.0– Rheumatic aortic stenosis with insufficiencyBB80.0– Rheumatic tricuspid valve stenosisBB81.0– Rheumatic tricuspid valve insufficiencyBB82.0– Rheumatic tricuspid valve stenosis with insufficiencyBB90.0– Rheumatic pulmonary valve stenosisBB91.0– Rheumatic pulmonary valve insufficiencyBB92.0– Rheumatic pulmonary valve stenosis with insufficiency
Exclusions from above levels
NE83.1– Infection arising from device, implant or graft, not elsewhere classified
Child codes
Sibling codes
Foundation entity
Acute rheumatic fever with heart involvement – http://id.who.int/icd/entity/535094176
Part of: 01: Certain infectious or parasitic diseases