1B41.2ICD-11 MMS 2026-01
Acute rheumatic myocarditis
Description
Acute rheumatic myocarditis is cardiac inflammation associated with acute rheumatic fever triggered by an autoimmune reaction to group A streptococci infection resulting in pancarditis involving inflammation of the myocardium, endocardium, and epicardium, usually with left-sided valvar involvement.
Index terms
- Acute rheumatic myocarditis
- active or acute rheumatic myocarditis
- active rheumatic fever with myocarditis
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- active rheumatic fibroid myocarditis
- active rheumatic interstitial myocarditis
- active rheumatic myocarditis
- active rheumatic progressive myocarditis
- acute or subacute rheumatic myocardial insufficiency
- acute rheumatic fever with myocarditis
- acute rheumatic toxic myocarditis
- chronic active rheumatic myocarditis
- old active rheumatic myocarditis
Exclusions from above levels
BB60.0– Rheumatic mitral valve stenosisBB61.0– Rheumatic mitral valve insufficiencyBB62.0– Rheumatic mitral valve prolapse
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BB63.0– Rheumatic mitral stenosis with insufficiencyBB70.0– Rheumatic aortic valve stenosisBB71.0– Rheumatic aortic valve insufficiencyBB72.0– Rheumatic aortic stenosis with insufficiencyBB80.0– Rheumatic tricuspid valve stenosisBB81.0– Rheumatic tricuspid valve insufficiencyBB82.0– Rheumatic tricuspid valve stenosis with insufficiencyBB90.0– Rheumatic pulmonary valve stenosisBB91.0– Rheumatic pulmonary valve insufficiencyBB92.0– Rheumatic pulmonary valve stenosis with insufficiencyNE83.1– Infection arising from device, implant or graft, not elsewhere classified
Sibling codes
Foundation entity
Acute rheumatic myocarditis – http://id.who.int/icd/entity/573695921
Part of: 1B41: Acute rheumatic fever with heart involvement › 01: Certain infectious or parasitic diseases