1B41.2

ICD-11 MMS 2026-01

Acute rheumatic myocarditis

Description

Acute rheumatic myocarditis is cardiac inflammation associated with acute rheumatic fever triggered by an autoimmune reaction to group A streptococci infection resulting in pancarditis involving inflammation of the myocardium, endocardium, and epicardium, usually with left-sided valvar involvement.

Index terms

  • Acute rheumatic myocarditis
  • active or acute rheumatic myocarditis
  • active rheumatic fever with myocarditis
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  • active rheumatic fibroid myocarditis
  • active rheumatic interstitial myocarditis
  • active rheumatic myocarditis
  • active rheumatic progressive myocarditis
  • acute or subacute rheumatic myocardial insufficiency
  • acute rheumatic fever with myocarditis
  • acute rheumatic toxic myocarditis
  • chronic active rheumatic myocarditis
  • old active rheumatic myocarditis

Exclusions from above levels

  • BB60.0 – Rheumatic mitral valve stenosis
  • BB61.0 – Rheumatic mitral valve insufficiency
  • BB62.0 – Rheumatic mitral valve prolapse
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  • BB63.0 – Rheumatic mitral stenosis with insufficiency
  • BB70.0 – Rheumatic aortic valve stenosis
  • BB71.0 – Rheumatic aortic valve insufficiency
  • BB72.0 – Rheumatic aortic stenosis with insufficiency
  • BB80.0 – Rheumatic tricuspid valve stenosis
  • BB81.0 – Rheumatic tricuspid valve insufficiency
  • BB82.0 – Rheumatic tricuspid valve stenosis with insufficiency
  • BB90.0 – Rheumatic pulmonary valve stenosis
  • BB91.0 – Rheumatic pulmonary valve insufficiency
  • BB92.0 – Rheumatic pulmonary valve stenosis with insufficiency
  • NE83.1 – Infection arising from device, implant or graft, not elsewhere classified

Sibling codes

  • 1B41.0 – Acute rheumatic pericarditis
  • 1B41.1 – Acute rheumatic endocarditis
  • 1B41.Y – Other acute rheumatic heart disease
  • 1B41.Z – Acute rheumatic heart disease, unspecified

Foundation entity

Acute rheumatic myocarditis – http://id.who.int/icd/entity/573695921

Part of: 1B41: Acute rheumatic fever with heart involvement › 01: Certain infectious or parasitic diseases