2A20.2

ICD-11 MMS 2026-01

Primary myelofibrosis

Index terms

  • Primary myelofibrosis
  • chronic idiopathic myelofibrosis
  • myelofibrosis NOS
Show allHide
  • Myelofibrosis with myeloid metaplasia
  • idiopathic myelofibrosis with myeloid metaplasia
  • megakaryocytic myeloid metaplasia
  • megakaryocytic myelosclerosis with myeloid metaplasia

Inclusions

  • chronic idiopathic myelofibrosis

Excludes

  • 2A60.38 – Acute panmyelosis with myelofibrosis

Exclusions from above levels

  • 2E03 – Malignant neoplasm metastasis in bone or bone marrow
  • http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
  • http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Sibling codes

  • 2A20.0 – Chronic myelogenous leukaemia, BCR-ABL1-positive
  • 2A20.1 – Chronic neutrophilic leukaemia
  • 2A20.3 – Chronic eosinophilic leukaemia, not elsewhere classified
  • 2A20.4 – Polycythaemia vera
  • 2A20.5 – Non mast cell myeloproliferative neoplasm, unclassifiable
  • 2A20.Y – Other specified non mast cell myeloproliferative neoplasms
  • 2A20.Z – Non mast cell myeloproliferative neoplasms, unspecified

Foundation entity

Primary myelofibrosis – http://id.who.int/icd/entity/336704235

Allowed postcoordination axes

Part of: 2A20: Non mast cell myeloproliferative neoplasms › 02: Neoplasms