2A21.10

ICD-11 MMS 2026-01

Urticaria pigmentosa

Index terms

  • Urticaria pigmentosa
  • Maculopapular cutaneous mastocytosis

Inclusions

  • Maculopapular cutaneous mastocytosis

Exclusions from above levels

  • 2E03 – Malignant neoplasm metastasis in bone or bone marrow
  • http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
  • http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Sibling codes

  • 2A21.1Y – Other specified cutaneous mastocytosis
  • 2A21.1Z – Cutaneous mastocytosis, unspecified

Foundation entity

Urticaria pigmentosa – http://id.who.int/icd/entity/245322245

Allowed postcoordination axes

Part of: 2A21.1: Cutaneous mastocytosis › 2A21: Mastocytosis › 02: Neoplasms