2A21.1ICD-11 MMS 2026-01
Cutaneous mastocytosis
Description
Cutaneous mastocytosis is characterised by abnormal accumulation and proliferation of cutaneous mast cells. Most types are isolated but cutaneous mastocytosis can occur in association with systemic disease. Clinical forms include cutaneous mastocytoma, urticaria pigmentosa (the most frequent form), pseudoxanthomatous nodular cutaneous mastocytosis, telangiectasia macularis eruptiva perstans and diffuse cutaneous mastocytosis.
Exclusions from above levels
2E03– Malignant neoplasm metastasis in bone or bone marrow- http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
- http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland
Child codes
Sibling codes
Foundation entity
Cutaneous mastocytosis – http://id.who.int/icd/entity/1300710062