2A80.3ICD-11 MMS 2026-01
Primary cutaneous follicle centre lymphoma
Description
A primary lymphoma of the skin composed of various numbers of small and large irregular neoplastic follicle center cells. Its morphologic pattern can be nodular, diffuse, or nodular and diffuse. It presents with solitary or grouped plaques and tumours, and it usually involves the scalp, forehead, or trunk. It rarely involves the legs. This type of cutaneous lymphoma tends to remain localised to the skin, and it has a favorable prognosis.
Index terms
- Primary cutaneous follicle centre lymphoma
Exclusions from above levels
- http://id.who.int/icd/entity/450630526 – Mature T-cell or NK-cell neoplasms
2E03– Malignant neoplasm metastasis in bone or bone marrow- http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
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- http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland
Sibling codes
2A80.0– Follicular lymphoma grade 12A80.1– Follicular lymphoma grade 22A80.2– Follicular lymphoma grade 32A80.4– Paediatric type follicular lymphoma2A80.5– Follicular lymphoma in situ2A80.6– Follicular lymphoma of small intestine2A80.Y– Other specified follicular lymphoma2A80.Z– Follicular lymphoma, unspecified
Foundation entity
Primary cutaneous follicle centre lymphoma – http://id.who.int/icd/entity/77501812