2A82.2

ICD-11 MMS 2026-01

Hairy-cell leukaemia

Description

A neoplasm of small B-lymphocytes with hairy projections in bone marrow, spleen, and peripheral blood. Most patients present with splenomegaly and pancytopenia.

Index terms

  • Hairy-cell leukaemia
  • HCL - [hairy cell leukaemia]
  • Hairy-cell leukaemia without mention of remission
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  • LRE - [leukemic reticuloendotheliosis]
  • Leukaemic reticuloendotheliosis
  • hairy-cell leukaemia, NOS
  • Hairy-c ell leukaemia in compete remission

Inclusions

  • Leukaemic reticuloendotheliosis

Exclusions from above levels

  • 2E03 – Malignant neoplasm metastasis in bone or bone marrow
  • http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
  • http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Sibling codes

  • 2A82.0 – Chronic lymphocytic leukaemia or small lymphocytic lymphoma
  • 2A82.1 – B-cell prolymphocytic leukaemia
  • 2A82.3 – Splenic B-cell lymphoma or leukaemia, unclassifiable
  • 2A82.Y – Other specified mature B-cell neoplasm with leukaemic behaviour
  • 2A82.Z – Mature B-cell neoplasm with leukaemic behaviour, unspecified

Foundation entity

Hairy-cell leukaemia – http://id.who.int/icd/entity/82152208

Allowed postcoordination axes

Part of: 2A82: Mature B-cell neoplasm with leukaemic behaviour › 02: Neoplasms