2A82.3

ICD-11 MMS 2026-01

Splenic B-cell lymphoma or leukaemia, unclassifiable

Description

A small B-cell clonal lymphoproliferative disorder of the spleen that does not fall into any of the other categories of mature B-cell neoplasms.

Index terms

  • Splenic B-cell lymphoma or leukaemia, unclassifiable
  • Hairy cell leukaemia-variant
  • Hairy cell leukaemia variant, provisional

Inclusions

  • Hairy cell leukaemia-variant

Exclusions from above levels

  • 2E03 – Malignant neoplasm metastasis in bone or bone marrow
  • http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
  • http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Sibling codes

  • 2A82.0 – Chronic lymphocytic leukaemia or small lymphocytic lymphoma
  • 2A82.1 – B-cell prolymphocytic leukaemia
  • 2A82.2 – Hairy-cell leukaemia
  • 2A82.Y – Other specified mature B-cell neoplasm with leukaemic behaviour
  • 2A82.Z – Mature B-cell neoplasm with leukaemic behaviour, unspecified

Foundation entity

Splenic B-cell lymphoma or leukaemia, unclassifiable – http://id.who.int/icd/entity/1475987117

Allowed postcoordination axes

Part of: 2A82: Mature B-cell neoplasm with leukaemic behaviour › 02: Neoplasms