2A82.3ICD-11 MMS 2026-01
Splenic B-cell lymphoma or leukaemia, unclassifiable
Description
A small B-cell clonal lymphoproliferative disorder of the spleen that does not fall into any of the other categories of mature B-cell neoplasms.
Index terms
- Splenic B-cell lymphoma or leukaemia, unclassifiable
- Hairy cell leukaemia-variant
- Hairy cell leukaemia variant, provisional
Inclusions
- Hairy cell leukaemia-variant
Exclusions from above levels
2E03– Malignant neoplasm metastasis in bone or bone marrow- http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
- http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland
Sibling codes
Foundation entity
Splenic B-cell lymphoma or leukaemia, unclassifiable – http://id.who.int/icd/entity/1475987117
Allowed postcoordination axes
Part of: 2A82: Mature B-cell neoplasm with leukaemic behaviour › 02: Neoplasms