2B03.0

ICD-11 MMS 2026-01

Primary cutaneous CD30-positive anaplastic large cell lymphoma

Description

An anaplastic large cell lymphoma that is limited to the skin at the time of diagnosis. Most patients present with solitary or localised skin lesions in a form of nodules or papules, which may be tumours. The t(2;5) translocation that is present in many cases of systemic anaplastic large cell lymphoma is not found in this disease.

Index terms

  • Primary cutaneous CD30-positive anaplastic large cell lymphoma
  • primary cutaneous CD30+ anaplastic large cell lymphoma
  • primary cutaneous CD30+ large T-cell lymphoma
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  • primary cutaneous anaplastic large-cell lymphoma

Exclusions from above levels

  • 2E08 – Skin infiltration by nodal or non-cutaneous extranodal lymphoma
  • 2E03 – Malignant neoplasm metastasis in bone or bone marrow
  • http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
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  • http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Sibling codes

  • 2B03.1 – Lymphomatoid papulosis

Foundation entity

Primary cutaneous CD30-positive anaplastic large cell lymphoma – http://id.who.int/icd/entity/1972636482

Allowed postcoordination axes

Part of: 2B03: Primary cutaneous CD30-positive T-cell lymphoproliferative disorders › 02: Neoplasms