2B03.1

ICD-11 MMS 2026-01

Lymphomatoid papulosis

Description

Lymphomatoid papulosis is a proliferation of T-cells, often clonal, characterised clinically by the appearance of crops of dome-shaped papules and nodules which tend to ulcerate and then heal with scarring.

Index terms

  • Lymphomatoid papulosis

Exclusions from above levels

  • 2E08 – Skin infiltration by nodal or non-cutaneous extranodal lymphoma
  • 2E03 – Malignant neoplasm metastasis in bone or bone marrow
  • http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
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  • http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Sibling codes

  • 2B03.0 – Primary cutaneous CD30-positive anaplastic large cell lymphoma

Foundation entity

Lymphomatoid papulosis – http://id.who.int/icd/entity/1791207220

Allowed postcoordination axes

Part of: 2B03: Primary cutaneous CD30-positive T-cell lymphoproliferative disorders › 02: Neoplasms