2B30.0

ICD-11 MMS 2026-01

Nodular lymphocyte predominant Hodgkin lymphoma

Description

Nodular lymphocyte predominant Hodgkin lymphoma (NLPHL) is characterised by a nodular, or a nodular and diffuse proliferation of scattered large neoplastic cells known as popcorn or lymphocyte predominant cells (LP cells) —formerly called L&H cells for lymphocytic and/or histiocytic Reed-Sternberg cell variants. At present an overlap between NLPHL and T-cell-rich large B-cell lymphoma cannot be excluded.

Index terms

  • Nodular lymphocyte predominant Hodgkin lymphoma
  • Hodgkin disease with diffuse lymphocytic predominance
  • Hodgkin disease with lymphocytic predominance
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  • Hodgkin disease with lymphocytic-histiocytic predominance
  • Hodgkin disease with nodular lymphocytic predominance
  • lymphocyte-rich Hodgkin lymphoma

Exclusions from above levels

  • 2E03 – Malignant neoplasm metastasis in bone or bone marrow
  • http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
  • http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Sibling codes

  • 2B30.1 – Classical Hodgkin lymphoma
  • 2B30.Z – Hodgkin lymphoma, unspecified

Foundation entity

Nodular lymphocyte predominant Hodgkin lymphoma – http://id.who.int/icd/entity/331115338

Allowed postcoordination axes

Part of: 2B30: Hodgkin lymphoma › 02: Neoplasms