2B30.0ICD-11 MMS 2026-01
Nodular lymphocyte predominant Hodgkin lymphoma
Description
Nodular lymphocyte predominant Hodgkin lymphoma (NLPHL) is characterised by a nodular, or a nodular and diffuse proliferation of scattered large neoplastic cells known as popcorn or lymphocyte predominant cells (LP cells) —formerly called L&H cells for lymphocytic and/or histiocytic Reed-Sternberg cell variants. At present an overlap between NLPHL and T-cell-rich large B-cell lymphoma cannot be excluded.
Index terms
- Nodular lymphocyte predominant Hodgkin lymphoma
- Hodgkin disease with diffuse lymphocytic predominance
- Hodgkin disease with lymphocytic predominance
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- Hodgkin disease with lymphocytic-histiocytic predominance
- Hodgkin disease with nodular lymphocytic predominance
- lymphocyte-rich Hodgkin lymphoma
Exclusions from above levels
2E03– Malignant neoplasm metastasis in bone or bone marrow- http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
- http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland
Sibling codes
Foundation entity
Nodular lymphocyte predominant Hodgkin lymphoma – http://id.who.int/icd/entity/331115338