2B54.0ICD-11 MMS 2026-01
Undifferentiated pleomorphic sarcoma of skin
Description
A rare malignant neoplasm arising from the skin. It is characterised by the presence of spindle cells in a storiform pattern and histiocytes with abundant cytoplasm.
Coding note from above levels
For use of this category, reference should be made to the mortality coding rules and guidelines in the Reference Guide.
Index terms
- Undifferentiated pleomorphic sarcoma of skin
- malignant fibrous histiocytoma of skin
- malignant fibrous histiocytoma of unspecified site
Inclusions
- malignant fibrous histiocytoma of skin
Exclusions from above levels
2A01.1– Mesenchymal tumour of meninges2A02.1– Tumours of cranial or paraspinal nerves- http://id.who.int/icd/entity/879154182 – Neoplasms of central nervous system or related structures
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- http://id.who.int/icd/entity/944754984 – Neoplasms of haematopoietic or lymphoid tissues
Sibling codes
Foundation entity
Undifferentiated pleomorphic sarcoma of skin – http://id.who.int/icd/entity/361875781
Allowed postcoordination axes
Part of: 2B54: Undifferentiated pleomorphic sarcoma, primary site › 02: Neoplasms