2B54

ICD-11 MMS 2026-01

Undifferentiated pleomorphic sarcoma, primary site

Description

Undifferentiated pleomorphic sarcoma is a high-grade sarcoma composed of pleomorphic spindled or epithelioid cells with no areas of differentiation that would indicate a specific subset of sarcoma.

Coding note from above levels

For use of this category, reference should be made to the mortality coding rules and guidelines in the Reference Guide.

Exclusions from above levels

  • 2A01.1 – Mesenchymal tumour of meninges
  • 2A02.1 – Tumours of cranial or paraspinal nerves
  • http://id.who.int/icd/entity/879154182 – Neoplasms of central nervous system or related structures
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  • http://id.who.int/icd/entity/944754984 – Neoplasms of haematopoietic or lymphoid tissues

Child codes

  • 2B54.0 – Undifferentiated pleomorphic sarcoma of skin
  • 2B54.1 – Undifferentiated pleomorphic sarcoma of retroperitoneum or peritoneum
  • 2B54.Y – Undifferentiated pleomorphic sarcoma, other specified primary site
  • 2B54.Z – Undifferentiated pleomorphic sarcoma, unspecified primary site

Sibling codes

  • 2B50 – Chondrosarcoma, primary site
  • 2B51 – Osteosarcoma, primary site
  • 2B52 – Ewing sarcoma, primary site
  • 2B53 – Fibroblastic or myofibroblastic tumour, primary site
  • 2B55 – Rhabdomyosarcoma, primary site
  • 2B56 – Angiosarcoma, primary site
  • 2B57 – Kaposi sarcoma, primary site
  • 2B58 – Leiomyosarcoma, primary site
  • 2B59 – Liposarcoma, primary site
  • 2B5A – Synovial sarcoma, primary site
  • 2B5B – Gastrointestinal stromal tumour, primary site
  • 2B5C – Endometrial stromal sarcoma, primary site
  • 2B5D – Malignant mixed epithelial mesenchymal tumour, primary site
  • 2B5E – Malignant nerve sheath tumour of peripheral nerves or autonomic nervous system, primary site
  • 2B5F – Sarcoma, not elsewhere classified, primary site
  • 2B5G – Myosarcoma of uterus, part not specified
  • 2B5H – Well differentiated lipomatous tumour, primary site
  • 2B5J – Malignant miscellaneous tumours of bone or articular cartilage of other or unspecified sites
  • 2B5K – Unspecified malignant soft tissue tumours or sarcomas of bone or articular cartilage of other or unspecified sites
  • 2B5Y – Other specified malignant mesenchymal neoplasms
  • 2B5Z – Malignant mesenchymal neoplasm of unspecified type

Foundation entity

Undifferentiated pleomorphic sarcoma, primary site – http://id.who.int/icd/entity/1348470541

Allowed postcoordination axes

Part of: 02: Neoplasms