2E81.10

ICD-11 MMS 2026-01

Disseminated lymphangiomatosis

Description

A rare disorder characterised by widespread proliferation of aberrant lymphatic vessels which typically infiltrate vital organs in the thorax and abdomen.

Index terms

  • Disseminated lymphangiomatosis
  • diffuse lymphangiomatosis
  • Diffuse lymphatic malformation (deprecated)
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  • Kaposiform lymphangiomatosis

Exclusions from above levels

  • LA90.1 – Lymphatic malformations
  • 2F20 – Pigmented naevus
  • 2F20.Y – Blue naevus

Sibling codes

  • 2E81.11 – Acquired progressive lymphangioma
  • 2E81.1Y – Other specified benign lymphatic neoplasms
  • 2E81.1Z – Benign lymphatic neoplasms, unspecified

Foundation entity

Disseminated lymphangiomatosis – http://id.who.int/icd/entity/913891613

Part of: 2E81.1: Benign lymphatic neoplasms › 2E81: Benign vascular neoplasms › 02: Neoplasms