LA90.1

ICD-11 MMS 2026-01

Lymphatic malformations

Description

Lymphatic malformations (LM), formerly referred to by the term lymphangioma, are malformations of the lymphatic system which result in obstructed lymphatic drainage. There are two types of LM: macrocystic LM (including cystic hygroma/lymphangioma) and tissue-infiltrating microcystic LM (lymphangioma circumscriptum). The macro and microcystic forms of LM may occur in association.

Exclusions from above levels

  • 2E81 – haemangioma and lymphangioma
  • LA13.5 – Congenital retinal aneurysm
  • LA8B.1 – Congenital anomaly of pulmonary arterial tree
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  • LA8C – Congenital anomaly of coronary artery
  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Child codes

  • LA90.10 – Macrocystic lymphatic malformation
  • LA90.11 – Microcystic lymphatic malformation
  • LA90.12 – Lymphatic malformations of certain specified sites
  • LA90.13 – Cystic hygroma in fetus
  • LA90.1Y – Other specified lymphatic malformations
  • LA90.1Z – Lymphatic malformations, unspecified

Foundation children elsewhere

  • BD93.0 – Primary lymphoedema

Sibling codes

  • LA90.0 – Capillary malformations
  • LA90.2 – Peripheral venous malformations
  • LA90.3 – Peripheral arteriovenous malformations
  • LA90.4 – Peripheral arterial malformations
  • LA90.5 – Pulmonary arteriovenous fistula
  • LA90.Y – Other specified structural developmental anomalies of the peripheral vascular system
  • LA90.Z – Structural developmental anomalies of the peripheral vascular system, unspecified

Foundation entity

Lymphatic malformations – http://id.who.int/icd/entity/1456264474

Allowed postcoordination axes

Part of: LA90: Structural developmental anomalies of the peripheral vascular system › 20: Developmental anomalies