3A01.1

ICD-11 MMS 2026-01

Neonatal vitamin B12 deficiency anaemia

Description

A disease caused by a lack of vitamin B12 in the mother, which is passed onto the fetus in the antenatal period or to the neonate during breast feeding. This disease is characterised by decreased levels of vitamin B12. This disease may present with increased risk of birth defects or preterm delivery, anaemia, irritability, failure to thrive or apathy. Confirmation is by identification of low levels of vitamin B12 in a blood sample.

Index terms

  • Neonatal vitamin B12 deficiency anaemia
  • Megaloblastic anaemia due to congenital non-hereditary vitamin B12 deficiency
  • Congenital nutritional vitamin B12 deficiency due to maternal vitamin B12 deficiency
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  • Nutritional vitamin B12 deficiency due to maternal vitamin B12 deficiency in breast-fed infants

Inclusions

  • Congenital nutritional vitamin B12 deficiency due to maternal vitamin B12 deficiency

Excludes

  • 3A01.0 – Hereditary vitamin B12 deficiency anaemia

Exclusions from above levels

  • 04 – Diseases of the immune system
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth or the puerperium
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  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations or chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes
  • http://id.who.int/icd/entity/1000704511 – Human immunodeficiency virus disease
  • JB64.1 – Other diseases of the blood or blood-forming organs or certain disorders involving the immune mechanism complicating pregnancy, childbirth or the puerperium

Sibling codes

  • 3A01.0 – Hereditary vitamin B12 deficiency anaemia
  • 3A01.2 – Vitamin B12 deficiency anaemia due to low intake
  • 3A01.3 – Vitamin B12 deficiency anaemia due to intrinsic factor deficiency
  • 3A01.4 – Vitamin B12 deficiency anaemia due to intestinal disease
  • 3A01.5 – Drug-induced vitamin B12 deficiency anaemia
  • 3A01.Y – Other specified megaloblastic anaemia due to vitamin B12 deficiency
  • 3A01.Z – Megaloblastic anaemia due to vitamin B12 deficiency, unspecified

Foundation entity

Neonatal vitamin B12 deficiency anaemia – http://id.who.int/icd/entity/1334119043

Part of: 3A01: Megaloblastic anaemia due to vitamin B12 deficiency › 03: Diseases of the blood or blood-forming organs