3A01.30

ICD-11 MMS 2026-01

Pernicious anaemia

Description

Acquired pernicious anaemia, also called Biermer's disease, is a disorder in vitamin B12 (cobalamin) absorption characterised by megaloblastic anaemia and gastrointestinal symptoms, and that can lead to neurological abnormalities.

Index terms

  • Pernicious anaemia
  • Biermer disease
  • Biermer-Addison disease
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  • Pernicious anaemia associated with other autoimmune disorders

Exclusions from above levels

  • 3A01.Y – Vitamin B12 deficiency anaemia due to congenital intrinsic factor deficiency
  • 04 – Diseases of the immune system
  • 05 – Endocrine, nutritional or metabolic diseases
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  • 18 – Complications of pregnancy, childbirth or the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations or chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes
  • http://id.who.int/icd/entity/1000704511 – Human immunodeficiency virus disease
  • JB64.1 – Other diseases of the blood or blood-forming organs or certain disorders involving the immune mechanism complicating pregnancy, childbirth or the puerperium

Sibling codes

  • 3A01.3Y – Other specified vitamin B12 deficiency anaemia due to intrinsic factor deficiency
  • 3A01.3Z – Vitamin B12 deficiency anaemia due to intrinsic factor deficiency, unspecified

Foundation entity

Pernicious anaemia – http://id.who.int/icd/entity/1493613976

Part of: 3A01.3: Vitamin B12 deficiency anaemia due to intrinsic factor deficiency › 3A01: Megaloblastic anaemia due to vitamin B12 deficiency › 03: Diseases of the blood or blood-forming organs