3A10.00

ICD-11 MMS 2026-01

Haemolytic anaemia due to glucose-6-phosphate dehydrogenase deficiency

Description

Glucose-6-phosphate dehydrogenase (G6PD) deficiency is the most common hereditary erythrocyte enzyme deficiency that can manifest with severe neonatal jaundice which can lead to serious neurological consequences, or, most often, with acute haemolytic anaemia following ingestion of certain foods (fava beans), common drugs (some antimalaria drugs, sulphamides, analgesics), or in the course of an infection, in otherwise asymptomatic individuals.

Index terms

  • Haemolytic anaemia due to glucose-6-phosphate dehydrogenase deficiency
  • Chronic non spherocytic anaemia
  • Favism
Show allHide
  • G6PD - [glucose-6-phosphate dehydrogenase deficiency] anaemia
  • Haemolytic anaemia due toG6PD deficiency
  • anaemia due to glucose-6-phosphate dehydrogenase deficiency
  • anaemia due to pentose phosphate pathway defect
  • favism anaemia
  • glucose-6-phosphate dehydrogenase deficiency anaemia
  • glucose-6-phosphate dehydrogenase deficiency with anaemia
  • pentose phosphate pathway disorder anaemia
  • Baghdad spring anaemia
  • Hereditary haemolytic nonspherocytic type 1 anaemia
  • anaemia due to haemolytic nonspherocytic (hereditary), type 1
  • haemolytic nonspherocytic type 1 anaemia

Exclusions from above levels

  • 04 – Diseases of the immune system
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth or the puerperium
Show allHide
  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations or chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes
  • http://id.who.int/icd/entity/1000704511 – Human immunodeficiency virus disease
  • JB64.1 – Other diseases of the blood or blood-forming organs or certain disorders involving the immune mechanism complicating pregnancy, childbirth or the puerperium

Sibling codes

  • 3A10.0Y – Other specified haemolytic anaemias due to hexose monophosphate shunt or glutathione metabolism anomalies
  • 3A10.0Z – Haemolytic anaemias due to hexose monophosphate shunt or glutathione metabolism anomalies, unspecified

Foundation entity

Haemolytic anaemia due to glucose-6-phosphate dehydrogenase deficiency – http://id.who.int/icd/entity/506935822

Part of: 3A10.0: Haemolytic anaemias due to hexose monophosphate shunt or glutathione metabolism anomalies › 3A10: Hereditary haemolytic anaemia › 03: Diseases of the blood or blood-forming organs