3A50.02

ICD-11 MMS 2026-01

Haemoglobin H disease (– α/– – included)

Description

Haemoglobin H (HbH) disease is a moderate to severe form of alpha-thalassemia characterised by pronounced microcytic hypochromic haemolytic anaemia.

Index terms

  • Haemoglobin H disease (– α/– – included)
  • HbH - [haemoglobin H] disease
  • alpha - /- - or mutational forms of alpha-thalassaemia
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  • alpha thalassaemia intermedia

Exclusions from above levels

  • KA85 – Hydrops fetalis due to haemolytic disease
  • 04 – Diseases of the immune system
  • 05 – Endocrine, nutritional or metabolic diseases
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  • 18 – Complications of pregnancy, childbirth or the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations or chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes
  • http://id.who.int/icd/entity/1000704511 – Human immunodeficiency virus disease
  • JB64.1 – Other diseases of the blood or blood-forming organs or certain disorders involving the immune mechanism complicating pregnancy, childbirth or the puerperium

Sibling codes

  • 3A50.00 – Mild alpha thalassaemia diseases
  • 3A50.01 – Thalassaemic alpha-chain variants
  • 3A50.03 – Hemoglobin Bart's fetalis syndrome
  • 3A50.0Y – Other specified alpha thalassaemia
  • 3A50.0Z – Alpha thalassaemia, unspecified

Foundation entity

Haemoglobin H disease (– α/– – included) – http://id.who.int/icd/entity/9436211

Part of: 3A50.0: Alpha thalassaemia › 3A50: Thalassaemias › 03: Diseases of the blood or blood-forming organs