3A80

ICD-11 MMS 2026-01

Congenital polycythaemia

Description

A disease caused by determinants occurring in the antenatal period leading to changes in the concentration of red blood cells. This disease is characterised by having a high concentration of red blood cells in the body leading to slow flow of blood. This disease may present with headaches, blurred vision, red skin, tiredness, high blood pressure, dizziness, periods of confusion, bleeding problems, gout or itchy skin. Confirmation is by identification of increased levels of red blood cells in a blood sample.

Exclusions from above levels

  • 04 – Diseases of the immune system
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth or the puerperium
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  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations or chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes
  • http://id.who.int/icd/entity/1000704511 – Human immunodeficiency virus disease
  • JB64.1 – Other diseases of the blood or blood-forming organs or certain disorders involving the immune mechanism complicating pregnancy, childbirth or the puerperium

Child codes

  • 3A80.0 – Primary inherited erythrocytosis
  • 3A80.Y – Other specified congenital polycythaemia
  • 3A80.Z – Congenital polycythaemia, unspecified

Foundation children elsewhere

  • KA8A – Polycythaemia neonatorum

Sibling codes

  • 3A81 – Acquired polycythaemia
  • 3A8Z – Polycythaemia, unspecified

Foundation entity

Congenital polycythaemia – http://id.who.int/icd/entity/1617675057

Part of: 03: Diseases of the blood or blood-forming organs