3B63.0

ICD-11 MMS 2026-01

Congenital thrombocytosis

Description

Familial thrombocytosis is a type of thrombocytosis, a sustained elevation of platelet numbers, which affects the platelet/megakaryocyte lineage and may create a tendency for thrombosis and haemorrhage but does not cause myeloproliferation.

Index terms

  • Congenital thrombocytosis
  • Familial thrombocythaemia
  • Hereditary thrombocythaemia
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  • Hereditary thrombocytosis
  • Autosomal dominant thrombocytosis
  • X-linked thrombocytosis

Inclusions

  • Hereditary thrombocytosis
  • Autosomal dominant thrombocytosis
  • X-linked thrombocytosis

Excludes

  • 3B63.1 – Essential thrombocythemia

Exclusions from above levels

  • JA43.3 – Postpartum coagulation defects
  • 04 – Diseases of the immune system
  • 05 – Endocrine, nutritional or metabolic diseases
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  • 18 – Complications of pregnancy, childbirth or the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations or chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes
  • http://id.who.int/icd/entity/1000704511 – Human immunodeficiency virus disease
  • JB64.1 – Other diseases of the blood or blood-forming organs or certain disorders involving the immune mechanism complicating pregnancy, childbirth or the puerperium

Sibling codes

  • 3B63.1 – Acquired thrombocytosis
  • 3B63.Y – Other specified thrombocytosis
  • 3B63.Z – Thrombocytosis, unspecified

Foundation entity

Congenital thrombocytosis – http://id.who.int/icd/entity/1695088249

Part of: 3B63: Thrombocytosis › 03: Diseases of the blood or blood-forming organs