3B64.14

ICD-11 MMS 2026-01

Thrombotic thrombocytopenic purpura

Description

This condition is idiopathic. This condition is characterised by abnormality of blood coagulation causing extensive microscopic clots to form in the small blood vessels throughout the body resulting in low platelet count. This condition may present with seizures, hemiplegia, paresthesias, visual disturbance, and aphasia or anaemia. Confirmation is by identification of thromboses.

Index terms

  • Thrombotic thrombocytopenic purpura
  • Moschcowitz disease
  • Moschcowitz syndrome
Show allHide
  • TTP - [thrombotic thrombocytopenic purpura]
  • Acquired thrombotic thrombocytopenic purpura due to anti-ADAMTS 13 antibodies
  • Congenital thrombotic thrombocytopenic purpura due to ADAMTS-13 deficiency
  • Upshaw-Schulman syndrome
  • congenital thrombocytopaenic purpura
  • Glomerular disorders in thrombotic thrombocytopenic purpura
  • Thrombotic thrombocytopenic purpura specified as refractory

Exclusions from above levels

  • JA43.3 – Postpartum coagulation defects
  • 04 – Diseases of the immune system
  • 05 – Endocrine, nutritional or metabolic diseases
Show allHide
  • 18 – Complications of pregnancy, childbirth or the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations or chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes
  • http://id.who.int/icd/entity/1000704511 – Human immunodeficiency virus disease
  • JB64.1 – Other diseases of the blood or blood-forming organs or certain disorders involving the immune mechanism complicating pregnancy, childbirth or the puerperium

Sibling codes

  • 3B64.10 – Immune thrombocytopenic purpura
  • 3B64.11 – Secondary thrombocytopenic purpura
  • 3B64.12 – Drug-induced thrombocytopenic purpura
  • 3B64.13 – Alloimmune thrombocytopenia
  • 3B64.1Y – Other specified acquired thrombocytopenia
  • 3B64.1Z – Acquired thrombocytopenia, unspecified

Foundation entity

Thrombotic thrombocytopenic purpura – http://id.who.int/icd/entity/1708277768

Part of: 3B64.1: Acquired thrombocytopenia › 3B64: Thrombocytopenia › 03: Diseases of the blood or blood-forming organs