4A01.20

ICD-11 MMS 2026-01

Immune dysregulation syndromes with hypopigmentation

Index terms

  • Immune dysregulation syndromes with hypopigmentation
  • Immunodeficiency syndromes with hypopigmentation

Exclusions from above levels

  • 02 – Neoplasms
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 20 – Developmental anomalies

Sibling codes

  • 4A01.21 – Immune dysregulation syndromes presenting primarily with autoimmunity
  • 4A01.22 – Immune dysregulation syndromes presenting primarily with lymphoproliferation
  • 4A01.23 – Primary haemophagocytic lymphohistiocytosis
  • 4A01.2Y – Other specified diseases of immune dysregulation
  • 4A01.2Z – Diseases of immune dysregulation, unspecified

Foundation entity

Immune dysregulation syndromes with hypopigmentation – http://id.who.int/icd/entity/2015243510

Part of: 4A01.2: Diseases of immune dysregulation › 4A01: Primary immunodeficiencies due to disorders of adaptive immunity › 04: Diseases of the immune system