4A01

ICD-11 MMS 2026-01

Primary immunodeficiencies due to disorders of adaptive immunity

Exclusions from above levels

  • 02 – Neoplasms
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 20 – Developmental anomalies

Child codes

  • 4A01.0 – Immunodeficiencies with predominantly antibody defects
  • 4A01.1 – Combined immunodeficiencies
  • 4A01.2 – Diseases of immune dysregulation
  • 4A01.3 – Other well-defined immunodeficiency syndromes due to defects in adaptive immunity
  • 4A01.Z – Primary immunodeficiencies due to disorders of adaptive immunity, unspecified

Sibling codes

  • 4A00 – Primary immunodeficiencies due to disorders of innate immunity
  • 4A0Y – Other specified primary immunodeficiencies
  • 4A0Z – Primary immunodeficiencies, unspecified

Foundation entity

Primary immunodeficiencies due to disorders of adaptive immunity – http://id.who.int/icd/entity/1169765917

Part of: 04: Diseases of the immune system