4A20.0

ICD-11 MMS 2026-01

Adult-onset immunodeficiency

Description

Adults with disseminated mycobacterial infections and/or other AIDS-defining infections, often involving concomitant neutrophilic dermatoses. All patients have high titres of anti-interferon-gamma and normal CD4 T helper cell counts.

Index terms

  • Adult-onset immunodeficiency

Exclusions from above levels

  • 02 – Neoplasms
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 20 – Developmental anomalies

Sibling codes

  • 4A20.1 – Acquired immunodeficiency due to loss of immunoglobulin
  • 4A20.2 – Secondary haemophagocytic lymphohistiocytosis
  • 4A20.Y – Other specified acquired immunodeficiencies
  • 4A20.Z – Acquired immunodeficiencies, unspecified

Foundation entity

Adult-onset immunodeficiency – http://id.who.int/icd/entity/1843843106

Part of: 4A20: Acquired immunodeficiencies › 04: Diseases of the immune system