4A20.2

ICD-11 MMS 2026-01

Secondary haemophagocytic lymphohistiocytosis

Exclusions from above levels

  • 02 – Neoplasms
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 20 – Developmental anomalies

Child codes

  • 4A20.20 – Haemophagocytic syndrome associated with infection
  • 4A20.21 – Haemophagocytic lymphohistiocytosis associated with a malignant disease
  • 4A20.2Y – Other specified secondary haemophagocytic lymphohistiocytosis
  • 4A20.2Z – Secondary haemophagocytic lymphohistiocytosis, unspecified

Sibling codes

  • 4A20.0 – Adult-onset immunodeficiency
  • 4A20.1 – Acquired immunodeficiency due to loss of immunoglobulin
  • 4A20.Y – Other specified acquired immunodeficiencies
  • 4A20.Z – Acquired immunodeficiencies, unspecified

Foundation entity

Secondary haemophagocytic lymphohistiocytosis – http://id.who.int/icd/entity/239985204

Allowed postcoordination axes

Part of: 4A20: Acquired immunodeficiencies › 04: Diseases of the immune system