4A40.00

ICD-11 MMS 2026-01

Systemic lupus erythematosus with skin involvement

Description

Systemic lupus erythematosus (SLE) involving the skin. This may present with a malar "butterfly" erythema or with extensive necrolysis of sun-exposed skin, particularly on the head, neck and upper torso.

Index terms

  • Systemic lupus erythematosus with skin involvement
  • Acute cutaneous lupus erythematosus
  • Systemic lupus erythematosus skin rash

Exclusions from above levels

  • 02 – Neoplasms
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 20 – Developmental anomalies

Sibling codes

  • 4A40.0Y – Other specified systemic lupus erythematosus
  • 4A40.0Z – Systemic lupus erythematosus, unspecified

Foundation entity

Systemic lupus erythematosus with skin involvement – http://id.who.int/icd/entity/757048800

Part of: 4A40.0: Systemic lupus erythematosus › 4A40: Lupus erythematosus › 04: Diseases of the immune system