4A41.01

ICD-11 MMS 2026-01

Juvenile dermatomyositis

Description

Juvenile dermatomyositis is the early-onset form of dermatomyositis, a systemic autoimmune inflammatory muscle disorder, characterised by proximal muscle weakness, evocative skin lesion, and systemic manifestations.

Index terms

  • Juvenile dermatomyositis
  • childhood type dermatomyositis
  • Hypomyopathic juvenile dermatomyositis
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  • Juvenile dermatomyositis with cutaneous vasculitis
  • Juvenile dermatomyositis with lipodystrophy
  • Juvenile dermatomyositis with myocarditis
  • Juvenile dermatomyositis with necrotising cutaneous vasculitis
  • Amyopathic juvenile dermatomyositis
  • Juvenile dermatomyositis with calcinosis
  • Juvenile dermatomyositis with overlap to nonorgan specific systemic autoimmune disorders
  • Juvenile myositis

Exclusions from above levels

  • 02 – Neoplasms
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 20 – Developmental anomalies

Sibling codes

  • 4A41.00 – Adult dermatomyositis
  • 4A41.0Z – Dermatomyositis, unspecified

Foundation entity

Juvenile dermatomyositis – http://id.who.int/icd/entity/1428089375

Allowed postcoordination axes

Part of: 4A41.0: Dermatomyositis › 4A41: Idiopathic inflammatory myopathy › 04: Diseases of the immune system