4A41

ICD-11 MMS 2026-01

Idiopathic inflammatory myopathy

Description

These comprise a diverse group of syndromes that have in common persistent muscle inflammation of unknown pathophysiology, resulting in damage that affects muscle function. The inflammatory muscle disease can either be acute or chronic in nature.

Exclusions from above levels

  • 02 – Neoplasms
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 20 – Developmental anomalies

Child codes

  • 4A41.0 – Dermatomyositis
  • 4A41.1 – Polymyositis
  • 4A41.2 – Inclusion body myopathy
  • 4A41.Y – Other specified idiopathic inflammatory myopathy
  • 4A41.Z – Idiopathic inflammatory myopathy, unspecified

Sibling codes

  • 4A40 – Lupus erythematosus
  • 4A42 – Systemic sclerosis
  • 4A43 – Overlap or undifferentiated nonorgan specific systemic autoimmune disease
  • 4A44 – Vasculitis
  • 4A45 – Antiphospholipid syndrome
  • 4A4Y – Other specified nonorgan specific systemic autoimmune disorders
  • 4A4Z – Nonorgan specific systemic autoimmune disorders, unspecified

Foundation entity

Idiopathic inflammatory myopathy – http://id.who.int/icd/entity/464294586

Part of: 04: Diseases of the immune system