4A43.21ICD-11 MMS 2026-01
Secondary Sjögren syndrome
Description
Secondary Sjögren syndrome is a progressive inflammatory autoimmune disease affecting the exocrine glands in the presence of other systemic autoimmune diseases, such as rheumatoid arthritis, systemic lupus erythematosus, and systemic sclerosis. Lymphocytic infiltrates replace functional epithelium, leading to oral and ocular dryness.
Index terms
- Secondary Sjögren syndrome
Exclusions from above levels
Sibling codes
Foundation entity
Secondary Sjögren syndrome – http://id.who.int/icd/entity/953143133
Allowed postcoordination axes
Part of: 4A43.2: Sjögren syndrome › 4A43: Overlap or undifferentiated nonorgan specific systemic autoimmune disease › 04: Diseases of the immune system